Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV004531559 | SCV004104864 | likely pathogenic | COL4A1-related disorder | 2023-07-10 | criteria provided, single submitter | clinical testing | The COL4A1 c.3851G>A variant is predicted to result in the amino acid substitution p.Gly1284Glu. To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating it is rare. This variant occurs at a glycine (Gly) residue within the highly conserved collagen triple helical domain (Gly-X-Y) were glycine variants are frequently pathogenic (Plaisier et al. 1993. PubMed ID: 20301768; https://www.ncbi.nlm.nih.gov/books/NBK7046/). This variant is classified as likely pathogenic. |