Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genomic Research Center, |
RCV000784946 | SCV000923489 | uncertain significance | Porencephaly 2 | 2019-01-01 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002536877 | SCV003298044 | uncertain significance | not provided | 2023-06-29 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. ClinVar contains an entry for this variant (Variation ID: 634465). This variant has not been reported in the literature in individuals affected with COL4A2-related conditions. This variant is present in population databases (rs772439696, gnomAD 0.007%). This sequence change replaces valine, which is neutral and non-polar, with methionine, which is neutral and non-polar, at codon 105 of the COL4A2 protein (p.Val105Met). |