Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV001328887 | SCV001520122 | uncertain significance | Bethlem myopathy 1A | 2019-05-05 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
Labcorp Genetics |
RCV001328887 | SCV003520083 | benign | Bethlem myopathy 1A | 2023-06-11 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002546283 | SCV003670768 | uncertain significance | Inborn genetic diseases | 2022-12-13 | criteria provided, single submitter | clinical testing | The c.1960G>A (p.E654K) alteration is located in exon 31 (coding exon 31) of the COL6A1 gene. This alteration results from a G to A substitution at nucleotide position 1960, causing the glutamic acid (E) at amino acid position 654 to be replaced by a lysine (K). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV003145576 | SCV003833786 | uncertain significance | not provided | 2019-02-06 | criteria provided, single submitter | clinical testing |