Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Medical Genetics, |
RCV004596013 | SCV005090974 | pathogenic | Bethlem myopathy 1B | 2024-05-10 | criteria provided, single submitter | clinical testing | PVS1, PS2, PM2 - This variant is expected to lead to a loss of protein function. It is absent from gnomAD. The variant was detected de novo (paternity confirmed). |
Al Jalila Children’s Genomics Center, |
RCV004798988 | SCV005420652 | likely pathogenic | Bethlem myopathy 1A | 2024-10-04 | criteria provided, single submitter | research | PVS1,PM2 |