Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV002227825 | SCV002506964 | uncertain significance | Marshall syndrome; Stickler syndrome type 2; Hearing loss, autosomal dominant 37 | 2021-05-07 | criteria provided, single submitter | clinical testing | The inherited c.1351-1G>A variant identified in the COL11A1 gene substitutes a Thymine for Cytosine at the -1 canonical splice position within intron 10/66. This variant is absent from gnomAD(v3.1.1) suggesting it is not a common benign variant in the populations represented in that database. This variant is absent from ClinVar and to our current knowledge has not been reported in affected individuals in the literature. The inherited c.1351-1G>A variant identified in the COL11A1 gene is reported as Variant of Uncertain Significance. |