Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV001334965 | SCV001527982 | uncertain significance | Fibrochondrogenesis 1 | 2018-03-22 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
Gene |
RCV001561099 | SCV001783634 | likely benign | not provided | 2020-09-29 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge; Canonical splice site variant with an unclear effect on protein function; Located in an alternatively spliced exon in which no variants have been reported in association with COL11A1-related disorders to date in the Human Gene Mutation Database (Stenson et al., 2014); This variant is associated with the following publications: (PMID: 32578940) |
Prevention |
RCV004531120 | SCV004752244 | likely benign | COL11A1-related disorder | 2019-10-23 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |