Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000694487 | SCV000822935 | pathogenic | Carnitine palmitoyl transferase 1A deficiency | 2020-07-07 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in CPT1A are known to be pathogenic (PMID: 16169268). This variant has been observed as homozygous in an individual and a cousin who are both affected with carnitine palmitoyltransferase 1A deficiency (PMID: 15110323, 16146704). ClinVar contains an entry for this variant (Variation ID: 65654). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Arg160*) in the CPT1A gene. It is expected to result in an absent or disrupted protein product. |
Fulgent Genetics, |
RCV000694487 | SCV002810298 | pathogenic | Carnitine palmitoyl transferase 1A deficiency | 2022-03-28 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV000694487 | SCV004211007 | pathogenic | Carnitine palmitoyl transferase 1A deficiency | 2023-03-25 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000694487 | SCV000086870 | not provided | Carnitine palmitoyl transferase 1A deficiency | no assertion provided | literature only |