Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001389641 | SCV001591074 | pathogenic | Arrhythmogenic right ventricular dysplasia 10 | 2021-05-27 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Gln558*) in the DSG2 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in DSG2 are known to be pathogenic (PMID: 23381804, 23911551). For these reasons, this variant has been classified as Pathogenic. This variant has been observed in individual(s) with right ventricular cardiomyopathy (PMID: 16505173). ClinVar contains an entry for this variant (Variation ID: 1075931). This variant is not present in population databases (ExAC no frequency). |