Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000197532 | SCV000252463 | uncertain significance | not provided | 2013-04-10 | criteria provided, single submitter | clinical testing | p.Gly407Arg (GGG>CGG): c.1219 G>C in exon 9 of the TYMP gene (NM_001953.3) The G407R missense substitution has not been published as a mutation, nor has it been reported as a benign polymorphism to our knowledge. Mutations in the TYMP gene are associated with the autosomal recessive disorder mitochondrial DNA depletion syndrome 1 (MNGIE Type). The amino acid change is non-conservative in that a small, uncharged Glycine residue is replaced by a large, positively charged Arginine residue. This change occurs at a highly conserved position in the TYMP protein. Multiple in-silico analysis programs predict that G407R is damaging to the TYMP protein. Based on the currently available information, it is unclear whether G407R is a disease-causing mutation or a rare benign variant. The variant is found in LSME-MITOP panel(s). |
Natera, |
RCV001828034 | SCV002081616 | uncertain significance | Mitochondrial neurogastrointestinal encephalomyopathy | 2021-07-28 | no assertion criteria provided | clinical testing |