Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002513094 | SCV003444611 | pathogenic | not provided | 2022-04-08 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with glutamine, which is neutral and polar, at codon 44 of the TYMP protein (p.Arg44Gln). For these reasons, this variant has been classified as Pathogenic. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt TYMP protein function. ClinVar contains an entry for this variant (Variation ID: 16661). This variant is also known as G435A. This missense change has been observed in individual(s) with mitochondrial neurogastrointestinal encephalomyopathy (PMID: 12177387). It has also been observed to segregate with disease in related individuals. This variant is not present in population databases (gnomAD no frequency). |
OMIM | RCV000018141 | SCV000038420 | pathogenic | Mitochondrial DNA depletion syndrome 1 | 2002-08-13 | no assertion criteria provided | literature only | |
Gene |
RCV000018141 | SCV000264498 | pathogenic | Mitochondrial DNA depletion syndrome 1 | 2016-01-14 | no assertion criteria provided | literature only |