Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003388740 | SCV004100492 | uncertain significance | Spinocerebellar ataxia type 19/22 | criteria provided, single submitter | clinical testing | The missense variant p.D295V in EEF2 (NM_001961.4) has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.D295V variant is novel (not in any individuals) in gnomAD Exomes and is novel (not in any individuals) in 1000 Genomes. The p.D295V missense variant is predicted to be damaging by both SIFT and PolyPhen2. The aspartic acid residue at codon 295 of EEF2 is conserved in all mammalian species. The nucleotide c.884 in EEF2 is predicted conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance |