Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002306300 | SCV002601364 | pathogenic | not provided | 2022-05-06 | criteria provided, single submitter | clinical testing | Reported as 6834del5 in an individual with atopic dermatitis (Zhang et al., 2011); Frameshift variant predicted to result in protein truncation, as the last 1783 amino acids are replaced with 39 different amino acids, and other loss-of-function variants have been reported downstream in HGMD.; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 21039602) |
Juno Genomics, |
RCV004796724 | SCV005417339 | likely pathogenic | Dermatitis, atopic, 2; Ichthyosis vulgaris | criteria provided, single submitter | clinical testing | PVS1_Strong+PM2_Supporting+PS4_Supporting+PP4 |