Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000657650 | SCV000779397 | pathogenic | not provided | 2025-02-21 | criteria provided, single submitter | clinical testing | Identified in individuals with either ichthyosis vulgaris or atopic dermatitis (PMID: 21039602, 21428977, 23290076); Nonsense variant predicted to result in protein truncation, as the last 1356 amino acids are lost, and other loss-of-function variants have been reported downstream in HGMD; This variant is associated with the following publications: (PMID: 23744309, 23290076, 21428977, 21326297, 36735214, 16444271, 21039602) |
Mendelics | RCV002248852 | SCV002516377 | pathogenic | Ichthyosis vulgaris | 2022-05-04 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV002248852 | SCV004049874 | pathogenic | Ichthyosis vulgaris | 2023-04-11 | criteria provided, single submitter | clinical testing | |
Juno Genomics, |
RCV004796265 | SCV005418696 | pathogenic | Dermatitis, atopic, 2; Ichthyosis vulgaris | criteria provided, single submitter | clinical testing | PM2_Supporting+PVS1_Strong+PS4+PP4 |