Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000479024 | SCV000568704 | uncertain significance | not provided | 2021-03-05 | criteria provided, single submitter | clinical testing | In silico analysis supports that this variant does not alter splicing; This variant is associated with the following publications: (PMID: 23634874, 30048824, 32126152, 30355306, 33144682) |
Athena Diagnostics | RCV000479024 | SCV004229676 | likely pathogenic | not provided | 2022-11-21 | criteria provided, single submitter | clinical testing | The frequency of this variant in the general population is consistent with pathogenicity (http://gnomad.broadinstitute.org). This variant has been identified in at least one individual with adult-onset Alexander disease. Assessment of experimental evidence suggests this variant results in abnormal RNA splicing and protein function (PMID: 23634874, 32126152). |
Gene |
RCV000192190 | SCV000223057 | not provided | Alexander disease | no assertion provided | literature only |