Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV003152823 | SCV003841265 | uncertain significance | Bryant-Li-Bhoj neurodevelopmental syndrome 1 | 2023-02-23 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. Missense changes are a common disease-causing mechanism. In silico tool predictions suggest damaging effect of the variant on gene or gene product (3Cnet: 0.74). A different missense change at the same codon (p.Thr46Ile) has been reported to be associated with H3-3A related disorder (ClinVar ID: VCV000985335 / PMID: 33268356). Therefore, this variant is classified as VUS according to the recommendation of ACMG/AMP guideline. |