Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV004792335 | SCV005414372 | uncertain significance | Bryant-Li-Bhoj neurodevelopmental syndrome 1 | 2024-11-11 | criteria provided, single submitter | clinical testing | |
Clinical Genomics Laboratory, |
RCV004792335 | SCV005685504 | uncertain significance | Bryant-Li-Bhoj neurodevelopmental syndrome 1 | 2024-10-25 | criteria provided, single submitter | clinical testing | The H3F3A c.388C>T (p.Arg130Cys) variant, to our knowledge, has not been reported in the medical literature. This variant is absent from the general population (gnomAD v.2.1.1), indicating it is not a common variant. Computational predictors are uncertain as to the impact of this variant on H3F3A function. Due to limited information, and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of this variant is uncertain at this time. |