Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Prof. |
RCV004819276 | SCV005439849 | uncertain significance | Autosomal dominant nonsyndromic hearing loss 56 | 2024-12-29 | criteria provided, single submitter | research | The TNC c.3297-3299delCAGinsAAT:p.(Gln1099Asn) heterozygous variant is very rare and predicted deleterious. It was detected in an individual with sloping mild-to-severe HL. |