Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004818849 | SCV005438745 | uncertain significance | Immunodeficiency 32B | 2023-07-22 | criteria provided, single submitter | clinical testing | The observed missense variant c.944G>Ap.Arg315His in IRF8 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Arg315His variant is absent in gnomAD Exomes. The amino acid Arg at position 315 is changed to a His changing protein sequence and it might alter its composition and physico-chemical properties. Multiple lines of computational evidence Polyphen-probably damaging, SIFT-damaging and Mutation Taster-disease causing predict a damaging effect on protein structure and function for this variant. The amino acid change p.Arg315His in IRF8 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |