Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001373653 | SCV001570380 | uncertain significance | Congenital muscular dystrophy due to integrin alpha-7 deficiency | 2024-08-13 | criteria provided, single submitter | clinical testing | This sequence change replaces serine, which is neutral and polar, with leucine, which is neutral and non-polar, at codon 558 of the ITGA7 protein (p.Ser558Leu). This variant is present in population databases (rs548594784, gnomAD 0.03%). This variant has not been reported in the literature in individuals affected with ITGA7-related conditions. ClinVar contains an entry for this variant (Variation ID: 1063777). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt ITGA7 protein function with a negative predictive value of 80%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Revvity Omics, |
RCV001373653 | SCV003815714 | uncertain significance | Congenital muscular dystrophy due to integrin alpha-7 deficiency | 2019-08-26 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004037580 | SCV003969238 | uncertain significance | not specified | 2023-04-24 | criteria provided, single submitter | clinical testing | The c.1673C>T (p.S558L) alteration is located in exon 12 (coding exon 12) of the ITGA7 gene. This alteration results from a C to T substitution at nucleotide position 1673, causing the serine (S) at amino acid position 558 to be replaced by a leucine (L). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |