Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
SIB Swiss Institute of Bioinformatics | RCV001731213 | SCV002500956 | uncertain significance | Muscular dystrophy, limb-girdle, autosomal recessive 27 | 2022-04-20 | criteria provided, single submitter | curation | This variant is interpreted as a variant of uncertain significance for Muscular dystrophy, limb-girdle, autosomal recessive 27. The following ACMG Tag(s) were applied: Absent from controls (or at extremely low frequency if recessive) in Exome Sequencing Project, 1000 Genomes Project, or Exome Aggregation Consortium (PM2); Multiple lines of computational evidence support a deleterious effect on the gene or gene product (PP3). |
OMIM | RCV001731213 | SCV001981622 | pathogenic | Muscular dystrophy, limb-girdle, autosomal recessive 27 | 2021-10-19 | no assertion criteria provided | literature only |