Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV000736033 | SCV001520182 | uncertain significance | Microcephaly, cataracts, impaired intellectual development, and dystonia with abnormal striatum | 2019-09-25 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
OMIM | RCV000736033 | SCV000864252 | pathogenic | Microcephaly, cataracts, impaired intellectual development, and dystonia with abnormal striatum | 2021-05-18 | no assertion criteria provided | literature only |