Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000456892 | SCV000549129 | pathogenic | Danon disease | 2020-02-12 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. While this particular variant has not been reported in the literature, truncating variants in LAMP2 are known to be pathogenic (PMID: 21415759). This sequence change creates a premature translational stop signal at codon 338 (p.Ser338*) of the LAMP2 gene. It is expected to result in an absent or disrupted protein product. |