Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004719976 | SCV005325531 | uncertain significance | not provided | 2023-08-29 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Functional studies showed that p.(T248I) does not significantly change protein levels or enzyme activity (Guo et al., 2016); Identified in a patient with aortic aneurysm in published literature (Guo et al., 2016); This variant is associated with the following publications: (PMID: 26838787) |
University of Washington Center for Mendelian Genomics, |
RCV000755143 | SCV000882965 | pathogenic | Congenital aneurysm of ascending aorta; Acute aortic dissection | 2016-01-12 | no assertion criteria provided | research |