Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003539792 | SCV000166498 | uncertain significance | not provided | 2016-11-18 | criteria provided, single submitter | clinical testing | This variant is present in population databases (rs587780769, ExAC 0.006%) but has not been reported in the literature in individuals with a EPCAM-related disease. ClinVar contains an entry for this variant (Variation ID: 136026). In summary, this is a rare missense change that is not predicted to affect protein function or cause disease. However, the evidence is insufficient at this time to prove that conclusively. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated, but these predictions have not been confirmed by published functional studies. This sequence change replaces threonine with serine at codon 192 of the EPCAM protein (p.Thr192Ser). The threonine residue is highly conserved and there is a small physicochemical difference between threonine and serine. |
Fulgent Genetics, |
RCV002498585 | SCV002813386 | uncertain significance | Congenital diarrhea 5 with tufting enteropathy; Lynch syndrome 8 | 2021-10-27 | criteria provided, single submitter | clinical testing |