Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001210729 | SCV001382230 | uncertain significance | Hypertrophic cardiomyopathy 14 | 2019-08-01 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C0"). This variant has not been reported in the literature in individuals with MYH6-related conditions. This variant is not present in population databases (ExAC no frequency). This sequence change replaces lysine with asparagine at codon 597 of the MYH6 protein (p.Lys597Asn). The lysine residue is weakly conserved and there is a moderate physicochemical difference between lysine and asparagine. |
Gene |
RCV002464411 | SCV002759276 | uncertain significance | not provided | 2022-12-01 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge; Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function |
Fulgent Genetics, |
RCV002484144 | SCV002791491 | uncertain significance | Hypertrophic cardiomyopathy 1; Dilated cardiomyopathy 1EE; Hypertrophic cardiomyopathy 14; Atrial septal defect 3; Sick sinus syndrome 3, susceptibility to | 2021-11-15 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004538453 | SCV004738464 | uncertain significance | MYH6-related disorder | 2024-02-07 | no assertion criteria provided | clinical testing | The MYH6 c.1791A>T variant is predicted to result in the amino acid substitution p.Lys597Asn. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.0065% of alleles in individuals of European (Non-Finnish) descent in gnomAD. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |