Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV002246185 | SCV002515883 | likely benign | Hypertrophic cardiomyopathy 14 | 2022-05-20 | criteria provided, single submitter | clinical testing | For the following reasons, the MYH6 sequence variant found is assessed by us as a "Liekely benign": the mutation has not been previously described in the specialized literature or listed in the HGMD and ClinVar databases; a comparison with the gnomAD browser did not provide evidence that this sequence change is a norm variant detectable also in non-affected individuals; the molecular diagnosis matches partial aspects of the patient's clinical symptoms; the mutation is independently classified as deleterious by four prediction programs. Based on the finding that the unaffected mother of index patient is a carrier and assuming complete penetrance, the sequence variants in MYH6- most likely represent rare familial variants. |