Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002544338 | SCV003498179 | uncertain significance | Hypertrophic cardiomyopathy 14 | 2023-05-05 | criteria provided, single submitter | clinical testing | This sequence change replaces glutamic acid, which is acidic and polar, with lysine, which is basic and polar, at codon 1118 of the MYH6 protein (p.Glu1118Lys). This variant is present in population databases (rs750174797, gnomAD 0.003%). This variant has not been reported in the literature in individuals affected with MYH6-related conditions. ClinVar contains an entry for this variant (Variation ID: 1328497). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt MYH6 protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV004988748 | SCV005451652 | uncertain significance | Cardiovascular phenotype | 2024-08-07 | criteria provided, single submitter | clinical testing | The p.E1118K variant (also known as c.3352G>A), located in coding exon 24 of the MYH6 gene, results from a G to A substitution at nucleotide position 3352. The glutamic acid at codon 1118 is replaced by lysine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be deleterious by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |
Joint Genome Diagnostic Labs from Nijmegen and Maastricht, |
RCV001796941 | SCV002037395 | uncertain significance | not provided | no assertion criteria provided | clinical testing | ||
Clinical Genetics DNA and cytogenetics Diagnostics Lab, |
RCV001796941 | SCV002038436 | uncertain significance | not provided | no assertion criteria provided | clinical testing |