Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001584685 | SCV001812663 | likely benign | not provided | 2020-12-23 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Labcorp Genetics |
RCV001584685 | SCV003266338 | likely benign | not provided | 2023-10-22 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002569110 | SCV003721270 | uncertain significance | Inborn genetic diseases | 2021-11-12 | criteria provided, single submitter | clinical testing | The c.1021C>T (p.R341W) alteration is located in exon 10 (coding exon 9) of the MYH9 gene. This alteration results from a C to T substitution at nucleotide position 1021, causing the arginine (R) at amino acid position 341 to be replaced by a tryptophan (W). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Prevention |
RCV004733366 | SCV005344429 | uncertain significance | MYH9-related disorder | 2024-05-27 | no assertion criteria provided | clinical testing | The MYH9 c.1021C>T variant is predicted to result in the amino acid substitution p.Arg341Trp. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.14% of alleles in individuals of Latino descent in gnomAD, including one homozygous individual, which may be too common to be causative. Although we suspect that this variant may be benign, at this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |