Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV004733899 | SCV005361728 | likely pathogenic | MYH9-related disorder | 2024-08-22 | no assertion criteria provided | clinical testing | The MYH9 c.130G>C variant is predicted to result in the amino acid substitution p.Ala44Pro. This variant was reported in two individuals with MYH9-related disease (Saposnik et al. 2014. PubMed ID: 25077172; Natesirinilkul et al. 2021. PubMed ID: 33855781; Niwa et al. 2024. PubMed ID: 38827217). This variant has not been reported in a large population database, indicating this variant is rare. This variant is interpreted as likely pathogenic. |