Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000562999 | SCV000662660 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-07-09 | criteria provided, single submitter | clinical testing | The p.D201G variant (also known as c.602A>G), located in coding exon 6 of the NBN gene, results from an A to G substitution at nucleotide position 602. The aspartic acid at codon 201 is replaced by glycine, an amino acid with similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Labcorp Genetics |
RCV000636721 | SCV000758161 | uncertain significance | Microcephaly, normal intelligence and immunodeficiency | 2025-02-03 | criteria provided, single submitter | clinical testing | This sequence change replaces aspartic acid, which is acidic and polar, with glycine, which is neutral and non-polar, at codon 201 of the NBN protein (p.Asp201Gly). This variant is present in population databases (rs587780098, gnomAD 0.003%). This variant has not been reported in the literature in individuals affected with NBN-related conditions. ClinVar contains an entry for this variant (Variation ID: 480015). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Gene |
RCV001568159 | SCV001791983 | uncertain significance | not provided | 2019-11-27 | criteria provided, single submitter | clinical testing | Not observed at a significant frequency in large population cohorts (Lek 2016); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect; Has not been previously published as pathogenic or benign to our knowledge |
Genome- |
RCV000636721 | SCV002045165 | uncertain significance | Microcephaly, normal intelligence and immunodeficiency | 2021-11-07 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV003470829 | SCV004199664 | uncertain significance | Aplastic anemia | 2023-05-16 | criteria provided, single submitter | clinical testing | |
Natera, |
RCV000636721 | SCV001460736 | uncertain significance | Microcephaly, normal intelligence and immunodeficiency | 2020-09-16 | no assertion criteria provided | clinical testing |