Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Fulgent Genetics, |
RCV002503300 | SCV002791765 | uncertain significance | Microcephaly, normal intelligence and immunodeficiency; Aplastic anemia; Acute lymphoid leukemia | 2022-05-14 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004945718 | SCV005455366 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-06-29 | criteria provided, single submitter | clinical testing | The p.K233Q variant (also known as c.697A>C), located in coding exon 6 of the NBN gene, results from an A to C substitution at nucleotide position 697. The lysine at codon 233 is replaced by glutamine, an amino acid with similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |