Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000811739 | SCV000952022 | pathogenic | not provided | 2025-01-23 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Glu210*) in the NTHL1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in NTHL1 are known to be pathogenic (PMID: 25938944, 26559593). This variant is present in population databases (no rsID available, gnomAD 0.002%). This variant has not been reported in the literature in individuals affected with NTHL1-related conditions. ClinVar contains an entry for this variant (Variation ID: 655543). For these reasons, this variant has been classified as Pathogenic. |
Ambry Genetics | RCV002363103 | SCV002660950 | pathogenic | Hereditary cancer-predisposing syndrome | 2024-08-12 | criteria provided, single submitter | clinical testing | The c.628G>T (p.E210*) alteration, located in exon 4 (coding exon 4) of the NTHL1 gene, consists of a G to T substitution at nucleotide position 628. This changes the amino acid from a glutamic acid (E) to a stop codon at amino acid position 210. This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. The NTHL1 c.628G>T alteration was flagged as a low confidence call in the Genome Aggregation Database (gnomAD). Based on the available evidence, this alteration is classified as pathogenic. |
Myriad Genetics, |
RCV003458215 | SCV004188351 | pathogenic | Familial adenomatous polyposis 3 | 2023-09-05 | criteria provided, single submitter | clinical testing | This variant is considered pathogenic. This variant creates a termination codon and is predicted to result in premature protein truncation. |
Baylor Genetics | RCV003458215 | SCV004192184 | likely pathogenic | Familial adenomatous polyposis 3 | 2023-02-12 | criteria provided, single submitter | clinical testing |