Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV000708807 | SCV000837793 | uncertain significance | Familial medullary thyroid carcinoma | 2018-07-02 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000804531 | SCV000944445 | uncertain significance | Hereditary insensitivity to pain with anhidrosis | 2025-01-13 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with cysteine, which is neutral and slightly polar, at codon 119 of the NTRK1 protein (p.Arg119Cys). This variant is present in population databases (rs757031354, gnomAD 0.002%). This variant has not been reported in the literature in individuals affected with NTRK1-related conditions. ClinVar contains an entry for this variant (Variation ID: 584595). Invitae Evidence Modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) indicates that this missense variant is not expected to disrupt NTRK1 protein function with a negative predictive value of 95%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Genome- |
RCV000804531 | SCV004048645 | uncertain significance | Hereditary insensitivity to pain with anhidrosis | 2023-04-11 | criteria provided, single submitter | clinical testing | |
Natera, |
RCV000804531 | SCV001454763 | uncertain significance | Hereditary insensitivity to pain with anhidrosis | 2020-09-16 | no assertion criteria provided | clinical testing |