Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Godley laboratory, |
RCV001249471 | SCV001252727 | likely pathogenic | Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 4 | 2020-05-18 | criteria provided, single submitter | clinical testing | This heterozygous deletion of exon 12 of PARN was found in germline in a patient with unclassifiable ILD diagnosed at age 56. The patient also displayed other phenotypic features such as intermittent thrombocytopenia and GERD with a small hiatal hernia. The telomere length was below the 1st percentile in lymphocytes. The following ACMG/AMP criteria were used: PVS1_strong, PS4_supporting, PM2. |