Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001576492 | SCV001803696 | likely benign | not provided | 2018-11-29 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001576492 | SCV002215544 | uncertain significance | not provided | 2021-09-16 | criteria provided, single submitter | clinical testing | This variant is present in population databases (rs776409973, ExAC 0.02%). This variant has not been reported in the literature in individuals affected with PDGFB-related conditions. ClinVar contains an entry for this variant (Variation ID: 1208241). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Not Available"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Not Available"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This sequence change replaces arginine with glutamine at codon 191 of the PDGFB protein (p.Arg191Gln). The arginine residue is moderately conserved and there is a small physicochemical difference between arginine and glutamine. |