Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV001335958 | SCV001529224 | pathogenic | Myeloproliferative disorder, chronic, with eosinophilia | 2018-07-06 | criteria provided, single submitter | clinical testing | This variant was determined to be pathogenic according to ACMG Guidelines, 2015 [PMID:25741868]. Both patients presented somatic overgrowth, hyperelastic and fragile skin, and progressive neurologic deterioration (particularly impaired short-term memory) with white matter lesions on brain imaging [PMID 25454926] Functional studies showed that the P584R change constitutively activate the receptor in the absence of ligand [PMID 26455322] |
Baylor Genetics | RCV000200957 | SCV004040695 | pathogenic | Skeletal overgrowth-craniofacial dysmorphism-hyperelastic skin-white matter lesions syndrome | 2023-03-28 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000200957 | SCV000255604 | pathogenic | Skeletal overgrowth-craniofacial dysmorphism-hyperelastic skin-white matter lesions syndrome | 2015-02-01 | no assertion criteria provided | literature only |