Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory Genomica, |
RCV001290203 | SCV001477293 | uncertain significance | Mandibular hypoplasia-deafness-progeroid syndrome | 2020-06-01 | criteria provided, single submitter | clinical testing | |
Precision Medicine Center, |
RCV001290203 | SCV002546239 | likely pathogenic | Mandibular hypoplasia-deafness-progeroid syndrome | criteria provided, single submitter | clinical testing | PS2 + PM2_Supporting + PP4 | |
Gene |
RCV004770007 | SCV005376253 | pathogenic | not provided | 2023-12-03 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 19296856, 36280868) |