Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000464281 | SCV000547510 | uncertain significance | Colorectal cancer, susceptibility to, 10 | 2025-01-20 | criteria provided, single submitter | clinical testing | This sequence change replaces isoleucine, which is neutral and non-polar, with valine, which is neutral and non-polar, at codon 325 of the POLD1 protein (p.Ile325Val). This variant is present in population databases (rs558345043, gnomAD 0.03%). This missense change has been observed in individual(s) with breast cancer (PMID: 32792570). ClinVar contains an entry for this variant (Variation ID: 407965). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV000565563 | SCV000671132 | likely benign | Hereditary cancer-predisposing syndrome | 2024-10-17 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Gene |
RCV001547140 | SCV001766775 | uncertain significance | not provided | 2023-11-14 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; Observed in an individual with breast cancer (PMID: 32792570); This variant is associated with the following publications: (PMID: 20951805, 32792570) |
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV001547140 | SCV002046784 | uncertain significance | not provided | 2021-03-26 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV000565563 | SCV002534719 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-12-21 | criteria provided, single submitter | curation | |
Baylor Genetics | RCV000464281 | SCV005056514 | uncertain significance | Colorectal cancer, susceptibility to, 10 | 2024-03-20 | criteria provided, single submitter | clinical testing |