Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001987683 | SCV002226667 | uncertain significance | Progressive sclerosing poliodystrophy | 2021-08-27 | criteria provided, single submitter | clinical testing | This sequence change replaces lysine with asparagine at codon 109 of the POLG protein (p.Lys109Asn). The lysine residue is weakly conserved and there is a moderate physicochemical difference between lysine and asparagine. This variant is not present in population databases (ExAC no frequency). This variant has not been reported in the literature in individuals affected with POLG-related conditions. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Mayo Clinic Laboratories, |
RCV004793645 | SCV005411146 | uncertain significance | not provided | 2023-07-13 | criteria provided, single submitter | clinical testing | BP4, PM2_moderate |