Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001899454 | SCV002130133 | uncertain significance | Progressive sclerosing poliodystrophy | 2023-09-08 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. ClinVar contains an entry for this variant (Variation ID: 1370922). Disruption of the initiator codon has been observed in individual(s) with Alpers syndrome (PMID: 31665838). This variant is present in population databases (no rsID available, gnomAD 0.01%). This sequence change affects the initiator methionine of the POLG mRNA. The next in-frame methionine is located at codon 78. |