Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Medical Genetics, |
RCV004596026 | SCV005091014 | likely pathogenic | Noonan syndrome-like disorder with loose anagen hair 2 | 2023-10-18 | criteria provided, single submitter | clinical testing | PS2, PM1, PM2 - Low frequency in gnomAD population databases. In silico prediction tools estimated that the variant could be damaging for the protein function/stracture. The variant was detected de-novo (paternity confirmed). |