Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000414079 | SCV000490741 | pathogenic | not provided | 2015-06-09 | criteria provided, single submitter | clinical testing | The c.1122_1123delCA variant was not observed in approximately 6,500 individuals of European and African American ancestry in the NHLBI Exome Sequencing Project, indicating it is not a common benign variant in these populations. The c.1122_1123delCA variant in the PRKAR1A gene causes a frameshift starting with codon Asparagine 374, changes this amino acid to a Lysine residue and creates a Stop codon at position 52 of the new reading frame, denoted p.Asn374LysfsX52. This variant is predicted to cause the loss of the last 8 correctresidues which are replaced with 51 incorrect residues. Although this variant has not beenpreviously reported to our knowledge, we interpret it as pathogenic. |