Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Tartaglia Lab, |
RCV001261416 | SCV001337685 | pathogenic | Heart, malformation of; Atypical behavior; Abnormal facial shape; Specific learning disability; Intellectual disability | 2020-04-01 | criteria provided, single submitter | research | |
Clinical Genetics Laboratory, |
RCV004697049 | SCV005198717 | pathogenic | not provided | 2022-05-27 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004697049 | SCV005326747 | pathogenic | not provided | 2024-01-02 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging gain of function effect (PMID: 32721402); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 32721402, 37463579) |
OMIM | RCV001264764 | SCV001443067 | pathogenic | Noonan syndrome 13 | 2020-11-09 | no assertion criteria provided | literature only |