Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001209513 | SCV001380950 | benign | Hereditary pancreatitis | 2022-10-05 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV001209513 | SCV002703063 | uncertain significance | Hereditary pancreatitis | 2022-07-01 | criteria provided, single submitter | clinical testing | The p.Q56* variant (also known as c.166C>T), located in coding exon 2 of the PRSS1 gene, results from a C to T substitution at nucleotide position 166. This changes the amino acid from a glutamine to a stop codon within coding exon 2. This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. However, loss of function of PRSS1 has not been clearly established as a mechanism of disease. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |