Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Otorhinolaryngology, |
RCV004698371 | SCV005199862 | likely pathogenic | Noonan syndrome | 2024-03-30 | criteria provided, single submitter | clinical testing | The c.184T>C variant is a missense variant in PTPN11 and has not been reported with suspected or confirmed Noonan syndrome in a population databases (gnomAD no frequency). This variant has been identified by our laboratory in one individual with clinical features of Noonan Syndrome and was absent from large population studies. This gain-of-function variant is expected to result in an disrupted protein product, and classified as likely pathogenic for Noonan syndrome based on the ACMG/AMP criteria. |