Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000681431 | SCV000808894 | uncertain significance | not provided | 2018-08-21 | criteria provided, single submitter | clinical testing | The G562V variant has not been published as pathogenic or been reported as benign to our knowledge. This variant is observed in 2/15304 (0.01%) alleles from individuals of African ancestry in large population cohorts (Lek et al., 2016). In-silico analyses, including protein predictors and evolutionary conservation, support a deleterious effect. However, the G562V variant is a conservative amino acid substitution, which is not likely to impact secondary protein structure as these residues share similar properties. Additional evidence is needed to clarify pathogenicity, including observation in a significant number of affected individuals, segregation data, and functional evidence. |
Labcorp Genetics |
RCV003768046 | SCV004674669 | uncertain significance | RASopathy | 2022-12-23 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt RAF1 protein function. ClinVar contains an entry for this variant (Variation ID: 561970). This variant has not been reported in the literature in individuals affected with RAF1-related conditions. This variant is present in population databases (rs746937683, gnomAD 0.01%). This sequence change replaces glycine, which is neutral and non-polar, with valine, which is neutral and non-polar, at codon 562 of the RAF1 protein (p.Gly562Val). |