Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001321092 | SCV001511907 | uncertain significance | not provided | 2023-07-07 | criteria provided, single submitter | clinical testing | This missense change has been observed in individual(s) with retinitis pigmentosa (PMID: 19074801). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. ClinVar contains an entry for this variant (Variation ID: 208304). This variant is present in population databases (rs375761633, gnomAD 0.009%). This sequence change replaces serine, which is neutral and polar, with leucine, which is neutral and non-polar, at codon 433 of the RBP3 protein (p.Ser433Leu). |
Clin |
RCV000206945 | SCV000244051 | uncertain significance | Retinitis pigmentosa 66 | 2013-06-27 | no assertion criteria provided | literature only |