Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000230068 | SCV000287767 | pathogenic | Gastrointestinal stromal tumor; Paragangliomas 4; Pheochromocytoma | 2024-10-02 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Arg91*) in the SDHB gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in SDHB are known to be pathogenic (PMID: 19454582, 19802898). This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with SDHB-related conditions. ClinVar contains an entry for this variant (Variation ID: 239427). For these reasons, this variant has been classified as Pathogenic. |
Section on Medical Neuroendocrinolgy, |
RCV000505337 | SCV000599496 | pathogenic | Hereditary pheochromocytoma-paraganglioma | no assertion criteria provided | research |