Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000460882 | SCV000554013 | pathogenic | Gastrointestinal stromal tumor; Paragangliomas 4; Pheochromocytoma | 2016-07-30 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This sequence change creates a premature translational stop signal at codon 147 (p.Tyr147*) of the SDHB gene. It is expected to result in an absent or disrupted protein product. While this particular variant has not been reported in the literature, truncating variants in SDHB are known to be pathogenic (PMID: 19802898, 19454582). |