Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004508414 | SCV005020150 | uncertain significance | Familial thoracic aortic aneurysm and aortic dissection | 2023-12-15 | criteria provided, single submitter | clinical testing | The p.K559Q variant (also known as c.1675A>C), located in coding exon 5 of the SKI gene, results from an A to C substitution at nucleotide position 1675. The lysine at codon 559 is replaced by glutamine, an amino acid with similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |